The lung in multi-system disease
Identifieur interne : 002480 ( Main/Exploration ); précédent : 002479; suivant : 002481The lung in multi-system disease
Auteurs : R. Dinwiddie [Royaume-Uni]Source :
- Paediatric Respiratory Reviews [ 1526-0542 ] ; 2000.
English descriptors
- KwdEn :
- Teeft :
- Abnormality, Acute chest syndrome, Airway, Airway obstruction, Bilateral, Blood vessels, Bronchiolitis obliterans, Bronchoalveolar lavage, Chest pain, Corticosteroid, Disease activity, Disease figure, Disease process, Dysautonomia, Erythematosis, Familial dysautonomia, Familial dysautonomia syndrome, Fibrosis, Harcourt publishers, Interstitial, Interstitial fibrosis, Interstitial lung disease, Langerhans cell histiocytosis, Long term, Lung, Lung damage, Lung disease, Lung fields, Lung function tests, Lung function tests show, Lung volume, Lung volumes, Lupus, Lupus erythematosis, Lymphangiomatosis, Multiorgan involvement, Opportunistic infection, Oral corticosteroids, Other agents, Other complications, Other systems, Pleural effusion, Pleural effusions, Pneumocystis carinii, Pulmonary fibrosis, Pulmonary hypertension, Pulmonary lymphangiomatosis, Pulmonary oedema, Recurrent aspiration, Respiratory symptoms, Respiratory tract, Sarcoidosis, Severe cases, Sickle cell disease, Significant morbidity, Spontaneous pneumothorax, Syndrome, Systemic, Systemic disease, Systemic lupus erythematosis, Younger children.
Abstract
Abstract: Lung involvement in multi-system disease is rare in children. When it does occur it is associated with significant morbidity and mortality. Auto-immune diseases such as systemic lupus erythematosis, scleroderma and acute rheumatic disease can cause major lung pathology. Chronic illness such as sickle cell disease, mucopolysaccharidosis or familial dysautonomia can result in long-term recurrent respiratory problems. Rare conditions such as sarcoidosis, pulmonary lymphangiomatosis or Langerhan’s histiocytosis occasionally result in major lung disease in this age group. The prognosis for all of these conditions is very variable depending on the severity of the disease itself and its response to treatment which often involves the use of oral corticosteroids or other powerful immuno-suppressants.
Url:
DOI: 10.1053/prrv.2000.0003
Affiliations:
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Dinwiddie</name><affiliation wicri:level="1"><country xml:lang="fr">Royaume-Uni</country><wicri:regionArea>Great Ormond Street Hospital for Children NHS Trust, Great Ormond Street, London, WC1N 3JH</wicri:regionArea><wicri:noRegion>WC1N 3JH</wicri:noRegion></affiliation></author></analytic><monogr></monogr><series><title level="j">Paediatric Respiratory Reviews</title><title level="j" type="abbrev">YPRRV</title><idno type="ISSN">1526-0542</idno><imprint><publisher>ELSEVIER</publisher><date type="published" when="2000">2000</date><biblScope unit="volume">1</biblScope><biblScope unit="issue">1</biblScope><biblScope unit="page" from="58">58</biblScope><biblScope unit="page" to="63">63</biblScope></imprint><idno type="ISSN">1526-0542</idno></series></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">1526-0542</idno></seriesStmt></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>auto-immune diseaes, systemic lupus, erythematosis, sickle cell disease, familial dysautonomia, sarcoidosis, pulmonary lymphangiomatosis, histiocytosis</term></keywords><keywords scheme="Teeft" xml:lang="en"><term>Abnormality</term><term>Acute chest syndrome</term><term>Airway</term><term>Airway obstruction</term><term>Bilateral</term><term>Blood vessels</term><term>Bronchiolitis obliterans</term><term>Bronchoalveolar lavage</term><term>Chest pain</term><term>Corticosteroid</term><term>Disease activity</term><term>Disease figure</term><term>Disease process</term><term>Dysautonomia</term><term>Erythematosis</term><term>Familial dysautonomia</term><term>Familial dysautonomia syndrome</term><term>Fibrosis</term><term>Harcourt publishers</term><term>Interstitial</term><term>Interstitial fibrosis</term><term>Interstitial lung disease</term><term>Langerhans cell histiocytosis</term><term>Long term</term><term>Lung</term><term>Lung damage</term><term>Lung disease</term><term>Lung fields</term><term>Lung function tests</term><term>Lung function tests show</term><term>Lung volume</term><term>Lung volumes</term><term>Lupus</term><term>Lupus erythematosis</term><term>Lymphangiomatosis</term><term>Multiorgan involvement</term><term>Opportunistic infection</term><term>Oral corticosteroids</term><term>Other agents</term><term>Other complications</term><term>Other systems</term><term>Pleural effusion</term><term>Pleural effusions</term><term>Pneumocystis carinii</term><term>Pulmonary fibrosis</term><term>Pulmonary hypertension</term><term>Pulmonary lymphangiomatosis</term><term>Pulmonary oedema</term><term>Recurrent aspiration</term><term>Respiratory symptoms</term><term>Respiratory tract</term><term>Sarcoidosis</term><term>Severe cases</term><term>Sickle cell disease</term><term>Significant morbidity</term><term>Spontaneous pneumothorax</term><term>Syndrome</term><term>Systemic</term><term>Systemic disease</term><term>Systemic lupus erythematosis</term><term>Younger children</term></keywords></textClass><langUsage><language ident="en">en</language></langUsage></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Abstract: Lung involvement in multi-system disease is rare in children. When it does occur it is associated with significant morbidity and mortality. Auto-immune diseases such as systemic lupus erythematosis, scleroderma and acute rheumatic disease can cause major lung pathology. Chronic illness such as sickle cell disease, mucopolysaccharidosis or familial dysautonomia can result in long-term recurrent respiratory problems. Rare conditions such as sarcoidosis, pulmonary lymphangiomatosis or Langerhan’s histiocytosis occasionally result in major lung disease in this age group. The prognosis for all of these conditions is very variable depending on the severity of the disease itself and its response to treatment which often involves the use of oral corticosteroids or other powerful immuno-suppressants.</div></front></TEI><affiliations><list><country><li>Royaume-Uni</li></country></list><tree><country name="Royaume-Uni"><noRegion><name sortKey="Dinwiddie, R" sort="Dinwiddie, R" uniqKey="Dinwiddie R" first="R." last="Dinwiddie">R. 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